Description The Metabolic Formula System A line of medical foods and formulas designed to meet the special nutrient needs of infants, children, and adults with inherited metabolic disorders requiring specific nutrition support tailored to their condition. Ross metabolic medical foods must be used under medical supervision. Calcilo XD® Idiopathic hypercalcemia, Williams syndrome* Osteopetrosis* Cyclinex® -1, Cyclinex® -2 Urea cycle disorders* (Arginase deficiency, Argininosuccinic acid lyase deficiency, Argininosuccinic acid synthetase deficiency, Carbamylphosphate synthetase deficiency, N-Acetylglutamate synthetase deficiency, Ornithine transcarbamylase deficiency) Hyperornithinemia-Hyperammonemia-Homocitrullinuria (HHH) syndrome Ornithine-delta aminotransferase deficiency (gyrate atrophy)* Glutarex® -1, Glutarex® -2 Glutaric aciduria type I* Ketoadipic aciduria* Hominex® -1, Hominex® -2 Homocystinuria (vitamin B6-nonresponsive)* Isomil® Galactosemias* (Isomil Powder only) Hyperlipoproteinemia type IIa I-Valex® -1, I-Valex® -2 Isovaleric acidemia* 3-Hydroxy-3-methylglutaric aciduria* 3-Methylcrotonylglycinuria* 3-Methylglutaconic aciduria* Ketonex® -1, Ketonex® -2 Beta-ketothiolase deficiency* Maple syrup urine disease* 3-Hydroxyisobutyric aciduria Phenex™ -1, Phenex™ -2, Phenex™ -2 Vanilla Hyperphenylalaninemia* Phenylketonuria* Pro-Phree® Any disease or disorder for which protein must be restricted or for which additional energy, minerals, and vitamins are needed Celiac disease Hereditary fructose intolerance* Hyperornithinemia-Hyperammonemia-Homocitrullinuria (HHH) syndrome* Lysinuric protein intolerance* Nonketotic hyperglycinemia* Propimex® -1, Propimex® -2 Methylmalonic acidemia (vitamin B12-nonresponsive)* Propionic acidemia* ProViMin® Abetalipoproteinemia, hypobetalipoproteinemia Cholestasis Chylothorax Chylous ascites Fatty acid oxidation defects (mitochondrial) Glutaric aciduria type II Glycogen storage disease types II, III, IV Hyperlipoproteinemia type I (fasting chylomicronemia) Lecithin:cholesterol acyltransferase deficiency Lipodystrophy, congenital Lymphangiectasis, intestinal Malabsorption of carbohydrate and/or fat Malonyl coenzyme A decarboxylase deficiency Neurologically handicapped patients with low energy needs Supplement for any patient who requires increased protein, minerals, and vitamins X-linked adrenoleukodystrophy RCF® Carbohydrate intolerance Disaccharidase deficiencies Glucose transport protein deficiency* Glycogen storage diseases types I, III, IV, V Pyruvate dehydrogenase complex deficiency* Seizure disorders requiring a ketogenic diet* Tyrex® -1, Tyrex® -2 Tyrosinemia type Ia Tyrosinemia type Ib Alcaptonuria Tyrosinemia type II* Tyrosinemia type III* ____________________________ "-1" products are for infants and toddlers. "-2" products are for children, adults, and pregnant women. * See The Ross Metabolic Formula System Nutrition Support Protocols, ed 4, 2001, Ross Products Division, Abbott Laboratories, Columbus, Ohio, for methods of management. For precautions in using products, refer to product labels.